Abstract

Congenital bronchobiliary fistula (CBBF) is a rare anomaly in which a fistulous opening exists between the biliary tract and the tracheobronchial tree. CBBF may be accompanied by many congenital anomalies, with biliary system anomalies being the most common. CBBF was also reported to be associated with esophageal atresia in one case and right diaphragmatic hernia in another case. However, as far as we have known, CBBF case accompanied by multiple congenital anomalies has not been reported previously. In this article, we firstly present a case of a neonatal CBBF, incidentally diagnosed intraoperatively, accompanied by multiple congenital anomalies, including congenital diaphragmatic hernia. Secondly, we present our conclusions and updates about CBBF based on what we have learned from both our case and the literature.

Cite as: Hüseynov M, Hakalmaz AE. Birçok konjenital anomalinin eşlik ettiği doğumsal bronkobiliyer fistül olgu sunumu. Çoc. Cer. Derg. 2021;35(1):41-4.