A rare tumour of childhood: Extrarenal retroperitoneal teratoid Wilms’
Gökhan Berktuğ Bahadır1, Hakan Taşkınlar1, Yasemin Yuyucu Karabulut2, Çağlar Çıtak3, Feramuz Demİr Apaydın4, Ali Naycı1
1Mersin Üniversitesi Tıp Fakültesi Hastanesi, Çocuk Cerrahisi Anabilim Dalı, Mersin
2Mersin Üniversitesi Tıp Fakültesi Hastanesi, Patoloji Anabilim Dalı, Mersin
3Mersin Üniversitesi Tıp Fakültesi Hastanesi, Çocuk Sağlığı ve Hastalıkları Anabilim Dalı, Çocuk Onkoloji Bilim Dalı, Mersin
4Mersin Üniversitesi Tıp Fakültesi Hastanesi, Radyoloji Anabilim Dalı, Mersin
Keywords: childhood, retroperitoneal, Wilms tumour, teratoma
Abstract
Extrarenal teratoid Wilms’ tumor (ERTWT) is a rare malignancy of childhood.
A three-year-old female girl was referred for suspected pelvic mass with the initial diagnosis of acute abdomen during laparotomy. Computed tomography revealed a horseshoe kidney and a pelvic mass. Mass was totally removed at laparotomy and histopathology revealed mature teratoma with mucinous epithelium, cartilaginous tissue and triphasic components (blastemal, epithelial and stromal) of Wilms’ tumour. The diagnosis was ERTWT while having WT-1 gene positivity and non- association with the horseshoe kidney. The patient was followed up for 18 months without any metastasis or recurrence.
ERTWT should be considered in the differential diagnosis of acute abdomen. The goal should be complete resection not to lead to increase in the stage and the risk group of the tumour.